Bronchiectasis in children is a syndrome caused by airway inflammation and infection leading to bronchial dilatation and fibrosis.
Common causes:
Infection: Protracted bacterial bronchitis, adenovirus, Bordetella
Immune deficiency
Aspiration: Reflux, unsafe swallow
Primary Ciliary Dyskinesia
Symptoms:
Chronic wet cough
Unusual sputum pathogens
Decreased lung function
Diagnosis & Management:
Immune screen, sweat test, CT scan (BAR), PCD testing
Monitoring: spirometry, cough/sputum swabs
Management: ACT, antibiotics, macrolides