Medical

Bronchiectasis in children is a syndrome caused by airway inflammation and infection leading to bronchial dilatation and fibrosis.

Common causes:

Infection: Protracted bacterial bronchitis, adenovirus, Bordetella

Immune deficiency

Aspiration: Reflux, unsafe swallow

Primary Ciliary Dyskinesia

Symptoms:

Chronic wet cough

Unusual sputum pathogens

Decreased lung function

Diagnosis & Management:

Immune screen, sweat test, CT scan (BAR), PCD testing

Monitoring: spirometry, cough/sputum swabs

Management: ACT, antibiotics, macrolides